Abstract: Provided are in vitro and in vivo methods for determining whether a patient with Fabry disease will respond to treatment with a specific pharmacological chaperone.

Abstract: An apparatus for injection molding products from a mass including at least natural mono or polymers, provided with at least one mold cavity (2) and a deaeration channel (10) at least partly surrounding the mold cavity (2), wherein, between the deaeration channel and the mold cavity an overflow (8) space is provided which, on the one side, is in communication with the deaeration channel and, on the other side, with the mold cavity (2).

Abstract: The present invention is directed to a sealing member for establishing a water resistant seal between two elements which includes a resilient gasket having opposed gasket surfaces for engagement between the two elements; and a water resistant coating applied to the gasket. The water resistant coating providing releasable adhesive sealing contact with at least one of the elements. The present invention is also directed to a method of making a gasket seal for an electrical box.

Abstract: Techniques are disclosed that efficiently support the querying of meta-data in XML documents. The techniques include efficiently identifying XML elements along each location step in an XPath query that satisfy range constraints on ordered meta-data. The techniques include generating an inheritance meta-data index in which actual meta-data levels are associated only with elements for which a value is explicitly specified and associating non-leaf nodes of the index structure with inherited meta-data levels and inheritance source nodes. The techniques may be used with navigation-based and join-based XPath evaluation strategies.

Abstract: A compound having the formula Y-A-Z, wherein: A is a phenyl group which is unsubstituted or substituted; Y and Z are substituents at adjacent positions on ring A; Y represents: Z represents: and wherein the remaining variables are as defined in the specification.

Abstract: A method of providing a linear drive with an axially play-free entrainment connection between at least one linearly travelling rod (5) and a guide unit able to be moved parallel thereto. Between a coupling member (26), projecting to the fore of the rod (5), of the guide unit and the terminal face (27) of the rod (5) adhesive (34) is applied and then the components are so screwed together that athwart the direction of displacement relative motion is still possible. Then the entire unit is shifted between its two terminal positions even prior to curing of the adhesive (34), the components then aligning themselves. After the adhesive is cured the screw connection is finally drawn tight.

Abstract: The invention relates to an anti-roll/pitch system for use in a vehicle, in which a first mass, for instance a cabin, is suspended to a second mass, for instance a chassis, by means of a bearing arm, which is pivotally connected to the second mass around a pivot axis, via spring means. The anti-roll/pitch system comprises means to adjust a point of application of a spring force acting on the bearing arm, so as to adjust a moment exerted by said spring force on said bearing arm to counteract a load exerted on the bearing arm by the first mass. The spring force is exerted on the bearing arm through a flexible, elongated member, such as a string or cable, which takes up little space when adjusting the point of application. The invention furthermore relates to a built-in unit and a vehicle, equipped with an anti-roll/pitch system according to the invention.

Abstract: A method for treating a spinal disc comprises the steps of: determining the integrity of the annulus by subjecting the annulus to a first pressure applied internally of the annulus; providing access to the nucleus pulposus through the annulus without removing any tissue from the annulus or from the nucleus pulposus; and sealably injecting curable biomaterial through the annulus access directly into the nucleus pulposus at a second pressure correlated with the first pressure. The integrity of the annulus may be determined by a pre-operative discogram using a contrast medium that has a viscosity substantially similar to the viscosity of the biomaterial to be injected. The curable biomaterial may be injected under a pressure sufficient to distract opposing vertebral bodies communicating with the disc space.

Abstract: The present invention refers to the use of a meter completely integrated on a single piece, totally covered and without contact with the exterior that incorporates a prepayment system and a more efficient method to control the electric energy supply and obtains excellent information from the meter by means of contactless intelligent cards.

Abstract: Template-fixed ?-hairpin peptidomimetics of the General Formula (I); wherein Z1 and Z2 are template-fixed chains of 4 and 6 or 5 and 7 ?-amino acid residues and salts thereof. They have CXCR4-antagonizing properties and can be used as medicaments. These ?-sheet peptidomimetics can be manufactured by a process which is based on a mixed solid- and solution phase synthetic strategy.

Abstract: The invention relates to a method for manufacturing at least partly plastic vehicle parts in a mold with at least one mold cavity, comprising the steps of: at least partly closing the mold, wherein the at least one mold cavity is brought in a first position by means of at least one movable wall part of the at least one mold cavity; introducing plastic into the at least one mold cavity; upon complete closure of the mold and/or movement of the at least one movable wall part, bringing the at least one mold cavity in a second position, the at least one mold cavity in the second position having a different volume than in the first position; all this in such a manner that by bringing the at least one mold cavity from the first into the second position, the plastic fills the respective mold cavity completely.

Abstract: The invention provides adducts comprising a carbon nanotube with covalently attached silane moieties, and methods of making such adducts. Examples of silane moieties include trimethoxysilane; hexaphenyldisilane; silylphosphine; 1,1,1,3,5,5,5-heptamethyltrisiloxane; polydimethylsiloxane, poly(N-bromobenzene-1,3-disulfonamide); N,N,N?,N?-tetrabromobenzene-1,3-disulfonamide; hexamethyldisilazane (HMDS); chlorotrimethylsilane (TMCS); trichloromethylsilane (TCMS); an alkyl(alkylamino)silane; a tri(alkoxy)silane; tert-butyldimethylsilane; monochloroaminosilane; dichloroaminosilane; trichloroaminosilane; and dimethylaminosilane.

Abstract: The present invention relates to a method for preparing a starch product, wherein an aqueous starch mixture containing 5-50% dsb amylose is provided and the starch mixture is heated to a high temperature of at least 170 C. The invention further relates to a product obtainable by such a method and to the use of such product in a variety of food applications.

Abstract: The present invention provides a removable electronic tag housing. The housing includes a base for supporting the electronic tag. A cover is removably attachable to the base and defines between the cover and the base a passageway for accommodating an elongate member. The base includes a deflectable latch for locking engagement with the cover. The cover includes an access opening adjacent the latch for insertion of a removal tool thereinto to release the latch permitting detachment of the cover from the base.

Abstract: There is described a process for the production of a multi-layer body (100) having a partially shaped first layer (3m), wherein it is provided that in the process a diffractive first relief structure (4) with a high depth-to-width ratio of the individual structure elements, in particular with a depth-to-width ratio of >0.3, is shaped in a first region (5) of a replication layer (3) of the multi-layer body (100) and the first layer (3m) is applied to the replication layer (3) in the first region (5) and in a second region (4, 6) in which the relief structure is not shaped in the replication layer (3), with a constant surface density, and the first layer (3m) is partially removed in a manner determined by the first relief structure so that the first layer (3m) is partially removed in the first region (5) or in the second region (4, 6) but not in the second region (4, 6) or in the first region (5) respectively.

Abstract: The invention relates to a sterilizing device (10) for sterilizing closures (16), such as lids and caps for containers, such as bottles and jars, which device comprises a housing (12), provided with a closure entry (14) for supplying closures, a closure exit (18) for discharging sterilized closures from the device, a sterilizing-agent feed (21) for feeding sterilizing agent into the device and a discharge (28; 30) for discharging used sterilizing agent, as well as pass-through means (20) for passing closures (16) through the housing (12), the pass-through means (20) comprising a non-rectilinear pass-through path (58) in the plane parallel to the main plane of the closures. A sterilizing method is also described.

Abstract: A product display unit (10) has a product support surface of selectively adjustable area. The unit comprises an attachment (13, 14) for securing to a support structure (15) and a cantilevered support member (11) extending from the attachment in a first length direction. A plurality of elongate support arms (23) extend lengthwise in a direction substantially perpendicular to said first length direction. Each support arm (23) is pivotably attached to the cantilevered support member for movement between a first position and a second position to vary the area of the product display unit available to support product. Each support arm may also be telescopically movable from the second position to a third position to further vary the product support area.

Abstract: The present invention provides for an electronic tag housing used to support electronic tags to an article with a shrink wrap tube. The present invention provides an electronic tag assembly, including a housing, having a base and a cover attachable to the base. The housing includes a cavity for supporting an electronic tag. A heat shrinkable tube is supported by the housing between the cover and attachable base.