Abstract: The invention relates to compounds for the treatment of ribosomopathies. In particular, it refers to compounds for the treatment of Shwachman-Diamond Syndrome (SDS) and other ribosomopathies, such as Diamond-Blackfan Anemia (DBA), X-linked dyskeratosiscongenita (DKC) and Treacher Collins syndrome (TCS).

Abstract: The invention relates to compounds for the treatment of ribosomopathies. In particular, it refers to compounds for the treatment of Shwachman-Diamond Syndrome (SDS) and other ribosomopathies, such as Diamond-Blackfan Anemia (DBA), X-linked dyskeratosiscongenita (DKC) and Treacher Collins syndrome (TCS).

Abstract: A device for rotary conversion of a web or sheet material by cooperating cylindrical tools. The tools are arranged in a cassette. A driving device connects with the tools for rotating them. The cassette with the tools is placed in an adaptive cassette receiver. The driving device includes a motor and is supported on the lid of the cassette receiver. The cassette is placeable in and removable from the cassette receiver and is secured there and the driving device is connected to the tools.

Abstract: The device for rotary converting a web or sheet matter equips a processing station arranged in a machine (2) particularly producing packagings by means of cylindrical tools (10, 11). These tools are arranged in a cassette (7) and rotated by a driving device (40) equipped with a motor (42). The cassette (7), coming from an extrinsic equipment to that which normally equips the machine (2), is placed in another so-called adaptive cassette (20), which is removable and secured to the driving device (40). The latter is arranged on the adaptive cassette (20).