Abstract: The present disclosure provides a recombinant adeno-associated vector comprising a codon-optimized sequence encoding CYP4V2 linked to selected gene expression regulatory sequences and its use in treating Bietti Crystalline Dystrophy (BCD).

Abstract: A GIS mechanical fault diagnosis method and the device are disclosed. The method includes: collecting vibration signals to be measured of various excitation sources of GIS in mechanical operation; performing wavelet packet-feature entropy vector extraction on the vibration signals to be measured, when it is determined that the vibration signals to be measured are abnormal according to standard vibration signals in the normal state; inputting the extracted wavelet packet-feature entropy vectors into the pre-trained BP neural network for GIS mechanical fault identification, and outputting the corresponding fault. The disclosure integrates the vibration signals under the action of various excitation sources, extracts the feature entropy vectors according to the entropy theory, and constructs and trains a BP neural network that can classify and recognize various GIS mechanical faults, so as to perform comprehensive and effective GIS mechanical faults diagnose.

Abstract: The present disclosure provides a recombinant adeno-associated vector comprising a codon-optimized sequence encoding CYP4V2 linked to selected gene expression regulatory sequences and its use in treating Bietti Crystalline Dystrophy (BCD).

Abstract: A tile or plate, includes: an upper plate (3) and a lower plate (4); wherein a plurality of heat conducting cavities (6) are uniformly provided between the upper plate (3) and the lower plate (4) via connecting ribs (5). A solar collection layer is provided on an upper surface of the tile or the plate. Two ends of the tile or the plate are connected with each of the plurality of the heat conducting cavities (6) via transverse connecting pipes (23, 37, 42). The transverse connecting pipes (23, 37, 42) of two neighboring tiles are connected by a ferrule (17) or a hose (36) to form an integrated circulation system. The tile or plate has a large day-lighting area and a high energy conversion rate.

Abstract: A GIS mechanical fault diagnosis method and the device are disclosed. The method includes: collecting vibration signals to be measured of various excitation sources of GIS in mechanical operation; performing wavelet packet-feature entropy vector extraction on the vibration signals to be measured, when it is determined that the vibration signals to be measured are abnormal according to standard vibration signals in the normal state; inputting the extracted wavelet packet-feature entropy vectors into the pre-trained BP neural network for GIS mechanical fault identification, and outputting the corresponding fault. The disclosure integrates the vibration signals under the action of various excitation sources, extracts the feature entropy vectors according to the entropy theory, and constructs and trains a BP neural network that can classify and recognize various GIS mechanical faults, so as to perform comprehensive and effective GIS mechanical faults diagnose.

Abstract: A tile or plate, includes: an upper plate (3) and a lower plate (4); wherein a plurality of heat conducting cavities (6) are uniformly provided between the upper plate (3) and the lower plate (4) via connecting ribs (5). A solar collection layer is provided on an upper surface of the tile or the plate. Two ends of the tile or the plate are connected with each of the plurality of the heat conducting cavities (6) via transverse connecting pipes (23, 37, 42). The transverse connecting pipes (23, 37, 42) of two neighboring tiles are connected by a ferrule (17) or a hose (36) to form an integrated circulation system. The tile or plate has a large day-lighting area and a high energy conversion rate.