Abstract: The invention relates a nutritional compositions comprising lipid, OSA starch, protein, an encapsulating agent and carbohydrates, wherein the composition comprises lipid-containing particles which have a lipid core and wherein said lipid core is coated with OSA starch, and wherein the lipid core and OSA starch coating comprise less than 4 wt % protein altogether and relates to the method of making the nutritional compositions and further relates to the nutritional composition for use in glycogen storage disease.

Abstract: The invention relates to an emulsified O/W composition comprising emulsified lipid and OSA starch wherein the dry weight ratio of OSA starch to lipid is in the range from 1:3 to 1:5 and wherein less than 4 wt % protein is present based on total dry weight of the emulsified O/W composition and relates to the nutritional composition comprising the emulsified O/W composition and to the method of making these compositions and further relates to a nutritional composition for use in glycogen storage disease.

Abstract: The invention relates to a liquid or gelled pasteurized or sterilized composition comprising free amino acids, calcium, a digestible carbohydrate, and preferably an indigestible carbohydrate, wherein the free amino acids are present in a concentration between 5 and 30 g/100 ml, and the dry weight of the total composition is at least 40 g/100 ml, and preferably lower than 60 g/100 ml. The composition may in particular be used in the treatment of a human suffering from a disorder selected from the group consisting of phenylketonuria, homocystinuria, maple syrup urine disease, tyrosinaemia, propionic acidaemia, methylmalonic acidaemia, isovaleric acidaemia, urea cycle disorders and glutaric aciduria.