Abstract: A primary object of the present invention is to provide a method of automatically changing a calling mode of a telephone having a program timer installed therein as a timer setting changes, wherein the program timer comprising an on/off item responsible for controlling an on/off of the program timer, a timer setting item responsible for setting a time slot of an activation of the program timer, and a calling mode item responsible for setting a plurality of ring types, so that when the program timer is on and the time slot has been set by the timer setting item, a microprocessor of the telephone will activate the ring type set by the calling mode item for informing of an incoming call within the time slot.

Abstract: This application provides methods of improving protein replacement therapy by combining protein replacement therapy with active site-specific chaperones (ASSC) to increase the stability and efficiency of the protein being administered. The application further provides compositions comprising the purified protein and an ASSC, and methods of treatment by administering the compositions.

Abstract: A method of enhancing the activity of lysosomal &agr;-Galactosidase A (&agr;-Gal A) in mammalian cells and for treatment of Fabry disease by administration of 1-deoxy-galactonojirimycin and related compounds.

Abstract: Method fore enhancing in a mammalian cell the activity of an enzyme associated with a lysosomal storage disorder by administering a competitive inhibitor of the enzyme in an amount effective to enhance the activity of the enzyme. Preferred compounds for use in the method are imino sugars and related compounds.

Abstract: Method for enhancing in a mammalian cell the activity of an enzyme associated with a lysosomal storage disorder by administering a competitive inhibitor of the enzyme in an amount effective to enhance the activity of the enzyme. Preferred compounds for use in the method are imino sugars and related compounds.

Abstract: Method for enhancing in a mammalian cell the activity of an enzyme associated with Gaucher Disease by administering a competitive inhibitor of glucocerebrosidase in an amount effective to enhance the activity of the enzyme. Preferred compounds for use in the method are imino sugars and related compounds. In particular, C8-12-alkyl derivatives of N-alkyl-deoxynojirimycin, isofagomine compounds, and calystegine compoiunds are effective to enhance glucocerebrosidase activity.

Abstract: Method for enhancing in a mammalian cell the activity of an enzyme associated with a lysosomal storage disorder by administering a competitive inhibitor of the enzyme in an amount effective to enhance the activity of the enzyme. Preferred compounds for use in the method are imino sugars and related compounds.

Abstract: Method fore enhancing in a mammalian cell the activity of an enzyme associated with a lysosomal storage disorder by administering a competitive inhibitor of the enzyme in an amount effective to enhance the activity of the enzyme Prefcrred compounds for use in the method are imino sugars and related compounds

Abstract: A method of enhancing the activity of lysosomal &agr;-Galactosidase A (&agr;-Gal A) in mammalian cells and for treatment of Fabry disease by administration of 1-deoxy-galactonojirimycin and related compounds.

Abstract: Method fore enhancing in a mammalian cell the activity of an enzyme associated with a lysosomal storage disorder by administering a competitive inhibitor of the enzyme in an amount effective to enhance the activity of the enzyme. Preferred compounds for use in the method are imino sugars and related compounds.

Abstract: A method of enhancing the activity of lysosomal &agr;-Galactosidase A (&agr;-Gal A) in mammalian cells and for treatment of Fabry disease by administration of 1-deoxy-galactonojirimycin and related compounds.

Abstract: This invention provides aqueous film-forming foamable (AFFF) compositions comprising one or more environmentally-friendly .alpha.-branched fluoroalkylcarbonyl group-containing surfactants.

Abstract: Briefly, in one aspect, the present invention provides compositions of open-chain, .alpha.-branched fluoroalkylcarbonyl fluorides, and derivatives thereof.

Abstract: This invention provides a method of preparing fluoropolymer utilizing one or more environmentally-friendly fluorinated emulsifiers comprising .alpha.-branched fluoroalkylcarbonyl moieties. Fluoropolymer emulsions comprising one or more environmentally-friendly fluorinated emulsifiers comprising .alpha.-branched fluoroalkylcarbonyl moieties are also disclosed.

Abstract: To provide a process for producing a carbohydrate or a glycoconjugate without forming any hydrolytic product of the remodeled sugar chain.A process for producing a carbohydrate or a glycoconjugate by a remodeling reaction in the presence of a glycosidase which performs the remodeling reaction in an aqueous medium containing a water-soluble ketone and/or dioxane. Examples of the glycosidase include endoglycosidases such as Endo-A. Examples of the ketone include acetone.

Abstract: A pointing device that enable an user to remotely control the position of a cursor (10) on the display means (20) of a computer or interactive TV (30) is disclosed. The cursor (10) on the display means (20) appears at the position pointed by the remote pointing device. The remote pointing device comprising a microprocessor based machine (30), display means (20), a cursor (10), pointing means (40), means for determining the position on the display means (20) pointed by the pointing means (40), and means for inputting into the microprocessor based machine (30) the position on the display means (20) pointed by the pointing means (40) as the position of the cursor (10). Two optical embodiments are described: the first one uses imaging devices (1150) and the second one uses light scopes (1400). Interactive monitors (1500) with capability of displaying invisible images and the methods of using the same are also described. Improved light scope (1400) are described as well.

Abstract: Neoglycoconjugates and new intermediates for the synthesis thereof are synthesized by use of Endo-.beta.-N-acetylglucosaminidase from Arthrobacter protophormiae (Endo-A) in a medium containing an organic solvent.

Abstract: Neoglycoconjugates and new intermediates for the synthesis thereof are synthesized by use of Endo-.beta.-N-acetylglucosaminidase from Arthrobacter protophormiae (Endo-A) in a medium containing an organic solvent.